Search on: MOSCHKOWITZ DISEASE 
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Descriptor English:   Purpura, Thrombotic Thrombocytopenic 
Descriptor Spanish:   Púrpura Trombocitopénica Trombótica 
Descriptor Portuguese:   Púrpura Trombocitopênica Trombótica 
Synonyms English:   Purpura, Thrombotic Thrombopenic
Moschkowitz Disease
Thrombotic Thrombocytopenic Purpura, Congenital
Thrombotic Thrombocytopenic Purpura, Familial  
Tree Number:   C15.378.100.802.687.680
C15.378.140.855.925.750.680
C15.378.925.850
C23.550.414.950.687.680
C23.888.885.687.687.680
Definition English:   An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE. 
History Note English:   1986; use PURPURA, THROMBOTIC THROMBOPENIC 1965-1985 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DH diet therapy
DT drug therapy EC economics
EM embryology EN enzymology
EP epidemiology EH ethnology
ET etiology GE genetics
HI history IM immunology
ME metabolism MI microbiology
MO mortality NU nursing
PS parasitology PA pathology
PP physiopathology PC prevention & control
PX psychology RA radiography
RI radionuclide imaging RT radiotherapy
RH rehabilitation SU surgery
TH therapy US ultrasonography
UR urine VE veterinary
VI virology  
Record Number:   12133 
Unique Identifier:   D011697 

Occurrence in VHL:
 

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